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Momof2Boys
01-10-2008, 12:32 AM
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We found out that something was wrong during one of the ultrasounds at around 25 weeks pregnant. The midwife referred us to a fetal specialist and he told us that the baby may have a large misshaped head, it could be just normal or it could be craniosynostosis. Right now the bones were too soft to know for sure but they will monitor him every month for cranial pressure. The next visit we decided to do a fetal MRI to have a clearer image and it showed nothing major was wrong with his brain but they were still unable to tell if the bones had fused. The next visit was going to give us a shock. At 36 weeks was a routine ultrasound to check for pressure and talk about possible C-section. The specialist came in and we decided that a C-section was our best option since they still were unsure what was going on with the baby’s head. Then he goes on to say that we should see if we could delivery him this week incase he needs medical attention sooner than later. They wanted to do an anmenio (sp) that day to see if his lungs were mature enough to deliver in four days. The neurosurgeon was called and he suggested that if the baby was not showing any signs of trouble then they could wait a few weeks. However, the ultrasound did show that the umbilical cord was wrapped around the baby’s neck. At that point I got scared and decided to do the anmenio (which everyone lied and it hurts!), we figure if he is born early he could only benefit from any medical attention he does need plus I would not be worrying about the cord being around his neck for the next 3 weeks. *Which a little info from the specialist, they do see this happen during the ultrasounds and never usual say anything to the mother since normally during birth it does not cause any harm.
The test showed his lungs were mature and it was up to us when to do the C-section. Right at 37 weeks (consider full term) on May 1, 2007 Justin Alan was born by C-section. When they pulled him out of me and hearing him cry I was so relieved and tears just started rolling down. Justin had a little flattening on the right back side of his head but it was barely noticeable and you could feel a ridge on the back. We were lucky to have such wonderful doctors during the pregnancy and they had lined us up with a Neurosurgeon who saw Justin at the hospital. Justin’s tone was low but he and was doing great and we went home after 3 days.
Our first visit with the NS was two weeks after Justin was born. He still was unsure if the bones had fused or if they just overlapped from being smashed inside of me. We were hoping for overlapping and we think the pediatrician thought the same thing. At one month Justin had a 3D CT scan done. He did great during the scan. I fed him a bottle and he was perfectly still. The scan did show that the oppipital bone did fuse on the right side which we later found out was the Lambdoidal suture – one of the rarest types of cranio. We did not think too much about his cranio between the ages of one to three months since Justin became colicky and we were doing our very best to help him and remain sane ourselves. At two months the pediatrician put Justin on Axid for reflux which helped the colic somewhat and we put him on Nutramigen formula. The spitting up/vomit was horrible, the naps never more than 20 minutes, and he would sleep the best at night in his car seat. We were always afraid that he was having pressure in his head but the doctors never seemed too concerned. Justin’s head shape did get worse between the ages of 2-3 months. His right side of his forehead was bulging slightly, right eye was smaller than the left, the right ear was down and more forward than the left, and the left back side of his head started to have an egg shape affect. From the research online they called it asymmetrical, which is exactly what it looked like; his head shape was growing from the right forehead to the left back of his skull. He also started to have a tilt to his head since the left side was overcompensating for his brain growth. Family and friends did not notice the difference in his appearance but months passed they could slowly see the affects cranio was having. At four months we met with the NS and the craniofacial surgeon. Justin’s head shape was getting worse and it would only get worse. Since Lambdoidal suture fusing early is rare they really don’t know the affects if not corrected. He was already showing signs of delay and began physical therapy to strengthen him up before surgery. He also saw an ophthalmologist to check his eyes for any sign of pressure which he had passed.
Surgery was decided to be done when he was five months old which was the longest wait of our lives. The night before surgery was difficult and we doubted ourselves if we are making the right decision putting him through such surgery. He was so happy and his appearance was not bad, he looked perfect to us. Then we told ourselves that we don’t know how bad his appearance will be if not corrected and what type of delays or cranial pressure could happen. The advantage of doing it so early will not only help correct the shape of his head but he will not remember anything later until we show him pictures and tell him his story with craniosynostosis.
Surgery was scheduled for October 22, 2007 – Justin was 5 ½ months old.
Day 1 - Handing him over to the nurse to take him back to the operating room was the hardest moment but hearing the words after 3 ½ hours of surgery from the doctors’ mouth that he did great were the most wonderful words. During surgery, the NS and craniofacial surgeon said that they could see his brain through the bones in his skull on the right side. The bones had thin out so much from his brain trying to grow but could not grow normally. Knowing that made us feel so much better on the decision to have the surgery for Justin and in good timing. I could not imagine what could have happened if it was not corrected, especially if he had fallen on his head. He is a very lucky little boy. The craniofacial surgeon also tried something new; she switched the bones, placing the bad side on the left side of his skull and good side where he was having so much pressure on the right. He did need some blood during the surgery and possibly more later. After almost two hours in recovery we finally were able to see Justin. Seeing your baby with tubes and in so much pain was heart braking. He was given some morphine but he was still very uncomfortable. Once he was transported to the PICU room, he looked so much more comfortable with the morphine and Tylenol given every as needed.
Day 2 -The next morning at 4 am his right eye was swollen shut and he was drinking small amounts of juice. By 9 am Justin did not need any more blood and was released to the step down unit once a room became available (which one never did and we stayed in PICU the entire time). All IV’s came out and was just connected to vital monitors which became annoying to us and to Justin. At 10 am I was able to hold Justin for the first time. I was nervous since the swelling was getting worse and I was afraid of hurting him. It was the first time holding him since handing him over to the nurse. The bandage also came off that morning and the incision looked good but was still oozing some blood. Throughout the day he was holding down his juice and formula very well and doing great. The morphine and Tylenol was going longer between dosages. By 7 pm the left eye had swollen shut.
Day 3 – peak of swelling, he did not look like himself. His skin was so tight and he looked like he had gained 10 lbs. That afternoon he had his first smile since the surgery and by 8 pm his eyes started to open.
Day 4 – Both eyes were slowly opening and the swelling had gone down. He was no longer on Morphine and the pain was starting to upset him. Justin was released by the afternoon and sent home with just Tylenol. It was scary bringing him home since we did not have the doctors or nurses around to help but we were glad to be home again. Justin ended up with an ear infection after getting home and within five days had his first two teeth. So it was hard to tell if he was uncomfortable from the surgery, ears or teeth. Once the swelling went down, his head shape looked great. It was still a little flat on the right side but the bulge on his forehead was gone. The incision had dissolvable stitches and the dissolvable screws in the back of his skull started to become more noticeable. Justin also started to sit up and hold his head up straight which he never did prior to surgery. We were very happy to see Justin doing well and happy again even though the night time sleeping was not so great.
Justin’s one month follow appointment was good, the sutures were still open and he will need to follow up every three months. His head shape will improve little by little as his brain grows and hopefully no other surgeries will be needed.
Justin is just over 2 months post-op and 8 months old now. The incision on the right side looks great but the left side is more noticeable and red since he had a little irritation from the stitches. His head shape looks good but his ears are still not even. Justin is having problems sleeping at night and his reflux has gotten worse. We have an appointment with a GI specialist next week to help figure out what is going on. Other than that he is improving in therapy, trying to do the army crawl and a very happy baby during the day. Justin’s follow-up with the NS is next month and he sees the ophthalmologist in March.
We are happy to have the surgery now behind us and so proud of Justin. He was so strong and brave for such a little boy to go through so much.
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mrs j
01-10-2008, 07:13 AM
Jamie, thankyou for your story, its always encouraging to read successfull outcomes. Justin is just a wee trooper, and i hope these other appointments work out well, and i hope he doesn't need further surgery. sorry he is not sleeping great for you, reflux is such a rotten thing to deal with, Bradley was a nightmare with his, but before you know it he will be running round the house,having commando crawling games with his big brother.xxx

xl1200c
01-10-2008, 08:35 AM
WOW, Justin is not the only one who is strong and brave. You guys are amazing as parents. You have faced so many challenges and worrying situations. Justin is truly blessed to have you. Thank you so much for sharing.

craniogramma
01-13-2008, 11:01 AM
We as parents find ourselves, from the moment of conception praying to God that we have happy and healthy babies. I was blessed with 3 beautiful, happy and healthy children. When they are born, you think you couldn't possibly love anyone any more than you love your children. When they grow up, you find your prayers shift to your grandchildren. The love you feel for them is just as strong as the love you feel for your own. I was once again blessed. I had 5 happy and healthy grandchildren. Then came Justin. We were once again blessed. He is the 6th grandchild. Just as happy as the rest of them, but not altogether healthy. I look back and realize now, that I was afraid to love him. I didn't hold him at 1st the way I held my other grandchildren. I was so scared something would happen to him. Not knowing anything about his "condition". I thought maybe if I didn't love him so much, it wouldn't hurt as much if something did happen to him. Well....I was wrong. Not only do I love him, but maybe just a tiny bit more because of what he was going through. I remember being at the hospital when Justin had his surgery. When she told me about how hard it was to hand Justin to the nurses, it brought back memories of my handing my own baby over for a biopsy. The feeling of helplessness is so overwhelming. My heart went out to her. Jamie was so upset, (understandably so...). She looked at me and said "he's been so happy lately, and now look what I've done to him". That broke my heart. I told her..."no...don't regret for a moment what's happening to him now. You are a good mom, and are doing what's best for your baby. Don't EVER regret that". When the Dr. came out and told us the extent of the damage, we were floored. It was a lot worse than they had anticipated. It was a miracle he had not, at the least, sufferd siezures, and possibly brain damage. So by him having surgery at that point in time was, plain and simple, a miracle. So...I dubbed Justin, "our little miracle baby". He is doing much better now. All you have to do is look at him, and he flashes those big baby blues, smiles, and shows off those dimples. I have to give thanks to my son and daughter-in-law. They are stronger than I had ever realized, and GOD couldn't have given my grandchildren better parents. I thank God every day for my children, they have grown up to be wonderful parents, and awesome people in general. I guess most of all...I thank God for Justin. God saw fit to give this little blessed life to them, because he knew they could take care of him. You know...first impressions can be so deceiving. I always thought Jamie to be a frail little thing. I didn't think she could handle something like this. But...I was wrong. Jamie and Cliff are extremely strong people. They did, and still are, handling the situation better than I could have ever imagined. I am so proud of them, and I feel my bond with my daughter-in-law is even stronger than ever. I thank God. He could not have picked a better mommy and daddy than Jamie and Cliff for Jacob and Justin. Actually...everyone here needs to be commended. The strength and love it takes to deal with something like this, is amazing. If only the world had more good people as there are here, we would be a heck of a lot better off. GOD bless you all

xl1200c
01-13-2008, 12:17 PM
Craniogramma,

What a beautiful expression of your point of view. I don't think I've ever seen anything quite like that here before. It is so kind of you to share.

mrs j
01-13-2008, 04:53 PM
Craniogramma, thankyou for sharing how you feel, you have brought tears to my eyes.x

Momof2Boys
01-13-2008, 06:30 PM
Thank you mom, from all of us.

Momof2Boys
03-08-2008, 01:26 PM
Justin saw the GI specialist in January. She order a PH Probe and UGI. The axid for the reflux was down graded from 4 ml 2x a day to 1 ml 2x a day. Once we lowered the dosage the spitting up stopped. Six weeks later the PH probe was never ordered and I decided not to put him through the test since he was doing better. The UGI was done and his results were normal. His follow appointment with the NS was wonderful. The NS said we should be very pleased with Justin's head shape when he gets older. The plates and screws should dissappear within a year. We don't go back to see the NS for 6 months now.
Justin's physical therapy is really doing wonders for him. At nine months he was crawling and cruising along the sofa. His head position stays center for 90% of the time and he has one more session of therapy and he is done. I never thought he would be as far as he is right now. I am so proud of him. I am so glad we started the therapy early and had the surgery done when we did. He is doing great and the incision is barely noticeable now.

mckennasmum
03-08-2008, 05:09 PM
wonderful story, but a bit early in the day to bring tears to my eyes!!!

Momof2Boys
09-11-2008, 05:32 PM
Hello everyone! I just wanted to update you on Justin. He is getting so big. He started walking last month, it took 4 months for him to get his balance, but now he is trying to run around the house. We are still struggling with tummy problems, I believe he has a milk and possible peanut allergy but waiting on insurance to get him tested.
Justin had his follow up appointment with the NS and CFS last month and we are having some issues with large bumps still in the back of his head. Both the doctors believe they are from the dissolvable plates they put in during surgery. They normally dissolved around 6-12 months but are seeing them up to 18 months post-op. Justin is 10 months post-op right now. It's weird cause the bumps will get big and then fade away. The appointment went well overall, we don't go back for another year, unless the bumps start to become worse. (I hope not.) The NS said they might go in before he enters school age and smooth the bumps out. I am hoping we don't have to do another surgery, no matter how minor it might be. To this day I am still so glad we did that surgery. :angel

evergreenmom
09-15-2008, 01:05 AM
I just came across this site searching for info...My 5 1/2 mos. old son has recently been diagnosed with Lambdoid synostosis (partial closure on left lambdoid suture). We meet with the Craniofacial Team at Children's Hospital in Seattle tomorrow a.m.
I really appreciate you and others sharing your story...we are just at the begining and trying to find out what we are in for...just really hoping our beautiful little guy will be o.k. after all of this. We are totally overwhelmed, but seeing that others have gotten through it and are doing o.k. gives us hope so- Thank You!!

P.S. Any advice would be greatly appreciated!!

AllyCat
09-16-2008, 01:57 AM
Evergreenmom...just saw your post here! You should post in the Welcome Mat. We'll all see it then.

Congratulations on your baby!

Sorry to hear you are on this journey. Please let us know how things went at your meeting with the CFS. Lambdoid is really rare. We have a few lambdoid moms here who will hopefully chime in. Don't feel you have to stick with one surgeon. Many get a second and even third opinion. But if you like the one you met that's great! Check the resources and surgery sections for info on how to choose.

Feel free to ask questions. We are here to help! And feel free to post photos of your little guy...we love baby pictures

Welcome!

evergreenmom
09-16-2008, 07:35 AM
Allycat-
Thanks so much- Yeah I just noticed the welcome mat- I'll post there when I get a chance...We are just at the begining here and still in a state of shock. I see your son just had his surgery- I hope he is doing well. Take Care

Momof2Boys
09-17-2008, 06:09 PM
Welcome Evergreenmom!
This site was my life saver at times. I learned much more about cranio from these wonderful parents than I would have from the doctors. Our doctors did great work, but they tend to leave out some info. Piece of advice - ask questions and write down your questions on paper when you go to the appointments. It is overwhelming and I always forgot what I wanted to ask. Stay strong mommy! Your little guy will be okay, and through this journey you will be okay too. We are all here for you for advice or to let out your frustrates and fears.

lukemominca
10-22-2008, 01:27 AM
Jamie,

I am glad you got through everything ok; Justin looks like a trooper, like all of our kids are. I was just curious...my son had ICP after his first cranio surgery and we had another surgery and he seems to be better. I wonder how much if any of my son's delays were/are related to the ICP he had. Other than some physical PT stuff, has Justin showed any other delays? My son has autism and has a slew of GI stuff, which can but is not always related to autism...don't want to throw that hot potato on you.

If you haven't already, make sure your local early start office is helping you with any costs, assessments for therapy.

Cute little guy!

Kristin

lukemominca
10-22-2008, 01:31 AM
Evergreen mom,
Meant to tell you that we used Children's Seattle for my son's second revision cranio surgery this last spring, they are amazing. Get second opinions or more if you want, but we came up from CA to work with them, exceptional team. We had Dr. Ellenbogen, Birgfeld and Hopper. Good luck with your journey, take it day by day and get rest when you can, mental, physical, etc...you're gonna need it!

Kristin