PDA

View Full Version : Craniofacial Syndromes



mommysbudbud
10-12-2007, 11:54 AM
Our son was 2 weeks old when the neonatologist told us that our 32 weeker had sagittal synostosis. His skull bones were overlapping along his sagittal suture. When our son was 7 weeks old, we were sent to see a plastic surgeon. He informed us that he could fix our son's head and explained the surgery. He said after the surgery our son would be fitted with a cranio helmet. Then he said he would cut our son's forehead and pull it forward. Honestly, when my husband and I walked out of the doctors office, we thought what in the heck is he talking about. Our son's forehead seemed fine to us. We then went to see a neurosurgeon and then to see a geneticist.
We had a genetics test done on our son for Crouzon Syndrome. That came back negative. The geneticist knew that our son had something so he had our son's blood tested for Pfeiffer Syndrome. Negative again. We were then told that these syndromes can be hard to detect. So his blood was sent to a different lab, came back negative again for both syndromes. We were informed that multiply cranio is ALWAYS a syndrome regardless.
In the meantime, I started to do research on Crouzon Syndrome and Pfeiffer Syndrome. My husband chose to not talk about it and felt any doctor must know what he is talking about. Wrong.
We then drove 4 hours away to meet with a craniofacial team. We saw pictures of the children that had these syndromes, before and after surgery. The team, which is made up of plastic surgeons, neurosurgeons, geneticist, and other doctors. We were amazed at their knowledge and most important...how many patients they have worked on in the past and present. They knew what they were doing. We knew that this was the team for us. Our son's coronals were fused half way up as well by 6 months old.
An example: We live in San Diego, our son's pediatrician has never heard of these syndromes. Our son had an apnea episode one morning and he was admitted into the hospital, doctors from all over came in to see him because they either had never heard of these syndromes or had read about them and had never actually seen someone with 'it'. When ever I have a syndrome related concern with my son, I take him to see his pediatrician, her only example of a syndrome is Down Syndrome so she compares my son to that. Sad. My son's syndrome is strictly cosmetic.
I know that craniosynostosis is a serious 'condition', but when dealing with a child with a craniofacial syndrome...it is a whole different ball game. I wish my son only had sagittal synostosis. I wish he would only need one or maybe 2 surgeries and life goes on. But it won't happen that way....it is not that simple. With every child with these syndromes, their is always something different. My son has a mild form of his syndrome. So when I read online and spoke to other families about their children, I thought well my son doesn't have that characteristic so he must not have a syndrome. At the end of the day, he still has a syndrome.
With these syndromes, at some point the mutated chromosome 'triggers' and while the face continues to grow, the midface stops. Like it or not, he will need several surgeries. No one can put a number on it. No one knows for sure. He had the surgery for a CVR, forehead advancement, and orbital advancement at 6 months of age. That was 19 months ago and his eyes have become a little prominent again. So he will probably need another orbital advancement again. The concern that his soft spots closing too soon or not closing is very real. Hydrocephalus is not uncommon in these children as well as sleep apnea.
Educate yourself, do the research...join support groups that have first hand experience in these syndromes. Find a good craniofacial team, not just a craniofacial team.
Their are a lot of resources out there. I am here to help. Ask me anything, if I don't know the answer then I will point you in the right direction.
Best wishes to anyone who is beginning their journey down this path. You are not alone.
Dawn

4myboys
10-12-2007, 04:40 PM
Thank you so much for your post. We went through all the testing for Crouzons and it came back negative. My son had his CVR in May and I anxiously await his follow up CT as I am wondering if his forehead will need to be redone. It is frustrating to go through all of it and find that so many in the medical community do not know anything about these syndromes. You do really have to advocate on behalf of your child to get answers and to educate. I will tell you because the waiting for results was so awful I learned how to find peace regardless of outcomes and I know he has made me a better person. Thanks again,
Jen

Jacksmum3
10-12-2007, 05:29 PM
I totally agree with you on this one, Jack has also had testing for all craniofacila related syndromes, the reson for this? Jack had Bicoronal, he had protruding eyes, he has a high narrow palete we as a family have short broad thumbs Jack also had slanted eyes, low hair line, has suffered slight hearing loss with fluid behind ear drum, and now his head has not grown for 2 years baring in mind he is only 3.5 years old. at birth he had exomphalos which he had surgery for. The umbilical cord was also only 14cm long so very short.
My genetasist feels there is possibly something and is wanting to see my emediate family for bloods to be taken from them too (due to the thumbs).
I would certainly recommend any parent with a child with a syndrome go to a Craniofacial centre where they deal with many of these children, these are the ones with the experience. There is no way they would leave a child with increasing ICP'S to wait for surgery they would have them in and perform a posterior vault to relieve this pressure then when the baby is strong enough and the bone is a bit more mature would perform CVR and FOA.
Annmarie xx

mommysbudbud
10-12-2007, 06:07 PM
I think that people just don't understand that ICP is a very serious situation. I worry about it, I worry about hydrocephalus every day with my son. That is why he goes in every 4 months for his eyes, to check the optic nerve. His neurosurgeon said that this is something to watch closely. So please for the sake of your child or children...don't let another day go by if you feel your child is having issues because of ICP or craniosynostosis. Not worth the long term effects that it could have on your child.

Also, multiple synostosis is a syndrome. Their are probably tons of craniofacial syndromes out there that are placed in groups because the doctors don't know what it is. For my son, the doctors go back and forth on Crouzons or Pfeiffers and my thought is....since he doesn't have a majority of the signs...what if he has one of those unknown syndromes.

We have been told that children/people with craniofacial syndromes are uninsurable. The only way to get insurance for them is to either go through your work's insurance or pay a very high premium. I am curious to see how many people have run into this situation. Hydrocephalus too, uninsurable. I have tried to get 'syndrome' taken off of my son's medical records in the event I wanted or needed to get my own private insurance.

Dawn (mommy to Cole, Crouzon-Pfeiffer Syndrome)

craniomommynbaby
10-12-2007, 09:28 PM
People diagnosed with a craniofacial syndrome are uninsurable? Wow! That is a scary thought. Maybe I should think again about the genetic testing.

cheryl2
10-12-2007, 10:45 PM
People diagnosed with a craniofacial syndrome are uninsurable? Wow! That is a scary thought. Maybe I should think again about the genetic testing.


We have been told that as well. We have always made sure during job changes and so on to always pay for cobra, so we never go without insurance. If you change jobs, and you let your insurance lapse even briefly, your insurance from your new job can deny coverage. They have to take you if you are already covered by another insurance company. Friends of ours have a 2 year old son with a heart condition. They changed jobs, and did not keep up with the insurance from the old job. The new insurance company won't cover their son. Nice system we have.

cheryl2
10-12-2007, 10:48 PM
Also, I'm not sure, but I don't think your child has to have a diagnosed syndrome to be denied coverage. If you get a new job, and don't have health insurance from your previous job, they can always deny you if they want, just like if you were self-employed and wanted to buy insurance for yourself and your family on your own.

mommysbudbud
10-13-2007, 01:08 PM
My husband has had job offers, making almost twice as what he currently makes. He doesn't take them. The medical benefits is what is keeping him at his current employment. Currently through my husband's job...we have great medical coverage. Pretty much everything is covered. My son's surgery and hospital stay was covered 100%. We love our son's cranio team.
So if my husband does change jobs, then we want to make sure that we have the same kind of health insurance. We want to try and stay with the same cranio team.

So if you go from one employer to another, you can use Cobra during the in between time? Like you quit one job and start another but your new job's health care doesn't start for 30 days or 60 days....you would use Cobra during that time before your new benefits kick in?

Anyone on Medicad or whatever it is called?

cheryl2
10-13-2007, 07:20 PM
Yes, that's what Cobra is for. You can get Cobra for up to 18 months I think. If your insurance at your new job doesn't start for a few months, you can pay for the same insurance plan you had from your previous job on your own. It's pretty expensive. We've had to do it twice. Once it was almost $1700/month, the last time it was $1200/month. Ouch. But we had to make sure Clara was always covered.

mommysbudbud
10-14-2007, 05:57 PM
I am confused, so with my husband's employment. $200 is withdrawn from his paychecks per month to pay for medical. His company pays around $2000 a month. So if we use COBRA, we would have to pay $2000+ a month until our benefits kick in at another job?
If so, yikes! We were under the impression that we would only have to pay $200 a month until then. Guess we better really research this then.

mommysbudbud
10-14-2007, 06:00 PM
Cheryl,
If my husband switched jobs, how would the new employer/health insurance know that our child has a syndrome?

cheryl2
10-14-2007, 09:57 PM
Hi Dawn,
I'm not sure if you'd pay the entire $2000, but it's definitely more than what your employer takes out of your check. As to how they would know if your child has a syndrome, I don't know. That's a good question. In my friend's case, the insurance company knew their son had a heart condition and would not insure him. I don't know how they found out. I can ask her. Good luck. It's not fair that people have to be tied to their jobs because of health insurance. Whoever solves the health insurance issues in the US should get a Nobel.

Tawnia
10-15-2007, 01:35 PM
Hi Dawn,
I'm not sure if you'd pay the entire $2000, but it's definitely more than what your employer takes out of your check. As to how they would know if your child has a syndrome, I don't know. That's a good question. In my friend's case, the insurance company knew their son had a heart condition and would not insure him. I don't know how they found out. I can ask her. Good luck. It's not fair that people have to be tied to their jobs because of health insurance. Whoever solves the health insurance issues in the US should get a Nobel.

This is one of those times I am glad to live in Canada. We pay $108 a month for our whole family for BC medical right now but soon that will be paid by DH's work and we will just pay thier benefit premium. Everything except cosmetic surgery is covered 100% under BC medical. Eyeglasses and Dental are covered 80% by his benefits. Prescriptions we pay for. But my daughter's surgery and care and all of that we didn't even have to think about.

Jacksmum3
10-15-2007, 07:15 PM
I still don't know how you guys cope with all the worry of medical insurance with everything else thats going on? So many people moan about the NHS here but if they had a child like ours and needed a very costly surgery and they had to pay or sort insurance then they would have something to moan about.
I have said it before sometimes I cannot even bother phoning insurance companies due to damage or lost items because it seems like hard work.
Good luck to you all in fighting them tho and good on you xx

mommysbudbud
10-15-2007, 09:36 PM
I think every country has their benefits and their drawbacks. Our current insurance covers everything except we have a copay for CT scans and health check ups...which is $25. I laid in the hospital for 55 days, pregnant and heavily medicated, gave birth to my son, he spent 28 days in the NICU and it didn't cost us anything. Thank goodness for my husband's medical benefits from his employer.
I know a family that lived in another country who had a son with Crouzon Syndrome. The medical system their was so slow, they would make appts but have to wait so long to be seen. Their son died a few months ago from something that would of been handled in a matter of days here in the U.S.. Imagine losing your 3 yr old son. Terrible. Poor little boy was hospitalized then sent home and told to come back at the next available appt which ended up being several weeks away. His health went down hill. The parent's were helpless. 3 weeks after he passed away, the parents were notified that their son's appt for testing was coming up.
I think I would take a expensive premium and get seen in a timely manner anyday over a overcrowded free health care system.